Ischemic stroke as the first manifestation of severe ventricular hypertrabeculation/non-compaction.

Right Ventricular Non-Compaction Cardiomyopathy in Children: Brief Review Literature

      Right ventricular non-compaction cardiomyopathy (RVNC) is a genetic heterogeneous cardiomyopathy. Despite the increasing number of RVNC cases, the classification and natural history of this disorder are not completely clear. Also, because the pathogenic non-compaction cannot be easily differentiated from normal trabeculations, it is usually hard to accurately measure the prevalence of RV ...

Stroke and Stroke-like Episodes in Muscle Disease

BACKGROUND Though not obvious at a first glance, myopathies may be associated with ischemic stroke. Stroke-like episodes resemble ischemic stroke only to some extent but are a unique feature of certain mitochondrial disorders with a pathogenesis at variance from that of ischemic stroke. Only limited data are available about ischemic stroke in pri-mary myopathies and the management of stroke-lik...

Genetic Testing Is Not Required for Diagnosing Left Ventricular Hypertrabeculation / Non-Compaction.

Left ventricular twist abnormalities in patients with left ventricular non-compaction. A cardiovascular magnetic resonance study

Background Current morphologic left ventricular (LV) non-compaction (LVNC) criteria seem to be still insufficient. The prevalence of borderline degree of LV hypertrabeculation is far more frequent than initially expected. LV twist and strain values are proposed as potential new functional parameters supplementing the classic morphologic LVNC criteria. The aim of this study was to assess diagnos...

Left Ventricular Non-Compaction Syndrome Misdiagnosed as Dilated Cardiomyopathy on Several Occasions, Presenting With Recurrent Stroke

A 57-year-old African American female with a history of ischemic cardiomyopathy and a recent stroke with no residual deficits presented with apraxia and confusion. Non-contrast CT scan of the head revealed multiple embolic strokes in both cerebral hemispheres. Transthoracic echocardiography raised the suspicion for increased trabecular meshwork in the left ventricle. Cardiac MRI confirmed the f...